Galactosidase alpha Rabbit Monoclonal antibody, Unconjugated
Artikelnummer:
EKL-AMRE02016
Produktübersicht
Artikelname:
Galactosidase alpha Rabbit Monoclonal antibody, Unconjugated
Artikelnummer:
EKL-AMRE02016
Hersteller Artikelnummer:
AMRe02016
Alternativnummer:
EKL-AMRE02016-50UL, EKL-AMRE02016-100UL
Hersteller:
EnkiLife
Wirt:
Rabbit
Kategorie:
Antikörper
Applikation:
IHC, IP, WB
Spezies Reaktivität:
Human
Konjugation:
Unconjugated
Alternative Synonym:
Alpha gal A, GALA, Galactosidase, alpha, GLA, Melibiase
Produktbeschreibung
Defects in GLA are the cause of Fabry disease (FD) [MIM:301500]. FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. The disease consists of an inborn error of glycosphingolipid catabolism.
Produkteigenschaften
Klonalität:
Monoclonal
Molekulargewicht:
Calculated MW: 49 kDa, Observed MW: 49 kDa
NCBI:
2717
UniProt:
P06280
Puffer:
50mM Tris-Glycine(pH 7.4), 0.15M NaCl, 40% Glycerol, 0.01% Sodium azide and 0.05% BSA
Reinheit:
Affinity Purified
Formulierung:
Liquid
Target-Kategorie:
GLA
Anwendungsbeschreibung
Application Verdünnung:
WB 1:500-1:1000,IHC 1:50-1:100,IP 1:20-1:50
