BCKDHB Antibody - N-terminal region

Artikelnummer: ASB-ARP58593_P050
Artikelname: BCKDHB Antibody - N-terminal region
Artikelnummer: ASB-ARP58593_P050
Hersteller Artikelnummer: ARP58593_P050
Alternativnummer: ASB-ARP58593_P050-25UL,ASB-ARP58593_P050-100UL
Hersteller: Aviva
Wirt: Rabbit
Kategorie: Proteine/Peptide
Applikation: WB
Spezies Reaktivität: Bovine, Canine, Equine, Human, Porcine, Rabbit, Rat
Immunogen: The immunogen is a synthetic peptide directed towards the N-terminal region of Human BCKDHB
Alternative Synonym: E1B, BCKDE1B, BCKDH E1-beta
Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. Alternative splicing at this locus results in transcript variants with different 3 non-coding regions, but encoding the same isoform.
Klonalität: Polyclonal
Konzentration: 0.5 mg/ml
Molekulargewicht: 23kDa
NCBI: 594
UniProt: Q5T2J3
Formulierung: Liquid. Purified antibody supplied in 1x PBS buffer with 0.09% (w/v) sodium azide and 2% sucrose.
Host: Rabbit
Target Name: BCKDHB
Sample Type: Thyroid tumor lysates
Antibody Dilution: 1.0ug/ml
Host: Rabbit
Target: BCKDHB
Positive control (+): Human Liver (LI)
Negative control (-): HepG2 Cell Lysate (HG)
Antibody concentration: 1ug/ml
BCKDHB Antibody - N-terminal region (ARP58593_P050) in Human Thyroid tumor using Western Blot