BCKDHB Antibody - N-terminal region
Catalog Number:
ASB-ARP58593_P050
- Images (3)
| Article Name: | BCKDHB Antibody - N-terminal region |
| Biozol Catalog Number: | ASB-ARP58593_P050 |
| Supplier Catalog Number: | ARP58593_P050 |
| Alternative Catalog Number: | ASB-ARP58593_P050-25UL,ASB-ARP58593_P050-100UL |
| Manufacturer: | Aviva |
| Host: | Rabbit |
| Category: | Proteine/Peptide |
| Application: | WB |
| Species Reactivity: | Bovine, Canine, Equine, Human, Porcine, Rabbit, Rat |
| Immunogen: | The immunogen is a synthetic peptide directed towards the N-terminal region of Human BCKDHB |
| Alternative Names: | E1B, BCKDE1B, BCKDH E1-beta |
| Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. Alternative splicing at this locus results in transcript variants with different 3 non-coding regions, but encoding the same isoform. |
|
|
Host: Rabbit Target Name: BCKDHB Sample Type: Thyroid tumor lysates Antibody Dilution: 1.0ug/ml |
|
|
Host: Rabbit Target: BCKDHB Positive control (+): Human Liver (LI) Negative control (-): HepG2 Cell Lysate (HG) Antibody concentration: 1ug/ml |
|
|
BCKDHB Antibody - N-terminal region (ARP58593_P050) in Human Thyroid tumor using Western Blot |
Product Guarantee and Expert Support
