Galactosidase alpha Rabbit Monoclonal Antibody, Unconjugated

Artikelnummer: EKL-AMRE85595
Artikelname: Galactosidase alpha Rabbit Monoclonal Antibody, Unconjugated
Artikelnummer: EKL-AMRE85595
Hersteller Artikelnummer: AMRe85595
Alternativnummer: EKL-AMRE85595-50UL,EKL-AMRE85595-100UL
Hersteller: EnkiLife
Wirt: Rabbit
Kategorie: Antikörper
Applikation: IHC, IP, WB
Spezies Reaktivität: Human
Konjugation: Unconjugated
Alternative Synonym: Alpha gal A, GALA, Galactosidase, alpha, GLA, Melibiase
Defects in GLA are the cause of Fabry disease (FD) [MIM:301500]. FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. The disease consists of an inborn error of glycosphingolipid catabolism.
Klonalität: Monoclonal
Molekulargewicht: Calculated MW: 49 kDa, Observed MW: 49 kDa
NCBI: 2717
UniProt: P06280
Puffer: Purified antibody in TBS with 0.05% sodium azide,0.05%BSA and 50% glycerol.
Reinheit: Affinity Purification
Formulierung: Liquid
Target-Kategorie: Galactosidase alpha
Application Verdünnung: WB 1:500-1:1000,IHC 1:50-1:100,IP 1:10-1:20