Galactosidase alpha Rabbit Monoclonal Antibody, Unconjugated
Catalog Number:
EKL-AMRE85595
Product Overview
Article Name:
Galactosidase alpha Rabbit Monoclonal Antibody, Unconjugated
Biozol Catalog Number:
EKL-AMRE85595
Supplier Catalog Number:
AMRe85595
Alternative Catalog Number:
EKL-AMRE85595-50UL,EKL-AMRE85595-100UL
Manufacturer:
EnkiLife
Host:
Rabbit
Category:
Antikörper
Application:
IHC, IP, WB
Species Reactivity:
Human
Conjugation:
Unconjugated
Alternative Names:
Alpha gal A, GALA, Galactosidase, alpha, GLA, Melibiase
Product Description
Defects in GLA are the cause of Fabry disease (FD) [MIM:301500]. FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. The disease consists of an inborn error of glycosphingolipid catabolism.
Product Properties
Clonality:
Monoclonal
Molecular Weight:
Calculated MW: 49 kDa, Observed MW: 49 kDa
NCBI:
2717
UniProt:
P06280
Buffer:
Purified antibody in TBS with 0.05% sodium azide,0.05%BSA and 50% glycerol.
Purity:
Affinity Purification
Form:
Liquid
Target:
Galactosidase alpha
Application Notes
Application Dilute:
WB 1:500-1:1000,IHC 1:50-1:100,IP 1:10-1:20