Galactosidase alpha Rabbit Monoclonal Antibody, Unconjugated

Catalog Number: EKL-AMRE85595
Article Name: Galactosidase alpha Rabbit Monoclonal Antibody, Unconjugated
Biozol Catalog Number: EKL-AMRE85595
Supplier Catalog Number: AMRe85595
Alternative Catalog Number: EKL-AMRE85595-50UL,EKL-AMRE85595-100UL
Manufacturer: EnkiLife
Host: Rabbit
Category: Antikörper
Application: IHC, IP, WB
Species Reactivity: Human
Conjugation: Unconjugated
Alternative Names: Alpha gal A, GALA, Galactosidase, alpha, GLA, Melibiase
Defects in GLA are the cause of Fabry disease (FD) [MIM:301500]. FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. The disease consists of an inborn error of glycosphingolipid catabolism.
Clonality: Monoclonal
Molecular Weight: Calculated MW: 49 kDa, Observed MW: 49 kDa
NCBI: 2717
UniProt: P06280
Buffer: Purified antibody in TBS with 0.05% sodium azide,0.05%BSA and 50% glycerol.
Purity: Affinity Purification
Form: Liquid
Target: Galactosidase alpha
Application Dilute: WB 1:500-1:1000,IHC 1:50-1:100,IP 1:10-1:20